People of any age need to consume the right nutrients in their diet to ensure proper nutrition. In a person with CSID, dietary restrictions may require life-long adherence to a strict sucrose-free diet. This can vary depending on symptoms, but foods high in sucrose should be avoided.
Foods high in a starch component (amylopectin) including cereals, breads, pastas, and potatoes may also need to be excluded, especially during the first years of life. Starch tolerance is generally improved after the age of 3–4 years, and rice starch and maize starch are easier to digest.
Taking a small amount of baker’s yeast along with sucrose-containing foods has been found to reduce symptoms. However, baker’s yeast has an unpleasant taste.
An alternative to traditional baker’s yeast is sacrosidase (Sucraid), a liquid preparation that is tasteless when mixed with water. Sacrosidase is an enzyme replacement therapy only available by prescription. Sucraid was originally approved by the US Food and Drug Administration (FDA) in 1998 for treating CSID. Studies indicate its effectiveness in reducing symptoms while allowing a less restrictive diet and more normal lifestyle.
If CSID is diagnosed it is reasonable to treat by any of these treatment methods. You will need to consult with your physician or dietitian to determine the proper treatment approach and how long it should be continued.
The Healthcare Team
Dietary management of malabsorption disorders like CSID can be challenging. Talk to your doctor and a registered dietitian about what foods may cause digestion problems. Ask about alternatives. Learn how to read food labels and what to avoid. Be aware of possible sugar content of medicines, if needed.
In children, challenges increase as they begin to exert more independence. As a parent or care provider you will want to work with your child’s doctor to understand the condition and related limitations. This will provide you with the knowledge and ability to manage the child’s symptoms and needs.
At any age, working together with your healthcare providers will help ensure that proper nutrition is maintained while at the same time keeping symptoms under control.
- US National Library of Medicine. Congenital sucrase-isomaltase deficiency. Genetics Home Reference. July 2008; Accessed 10/08.2014.
- NASPGHAN and NASPGHAN Foundation for Children’s Digestive Health and Nutrition. Recognition and management of dietary carbohydrate-induced diarrhea in pediatric patients. Monographs. October 2011; . Accessed 10/08/2014.
- Puntis JWL, Zamvar V. Congenital sucrose-isomaltase deficiency: diagnostic challenges and response to enzyme replacement therapy. Arch Dis Child 2015;100:869-871
- Treem WR. Clinical aspects and treatment of congenital sucrose-isomaltase deficiency. J Pediatr Gastroenterol Nutr. 2012 Nov;55 Suppl 2:S7-13
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